Weston Hurst syndrome
Weston-Hurst syndrome is an exceptional variant of acute disseminated encephalomyelitis (ADEM) characterized by brain hemorrhages. Lesions are usually supratentorial and death is a usual outcome. Bonduelle et al. from the Department of Neurology, Bordeaux University Hospital, Neurosurgery, Clinique Navarre, Pau, France, report a cerebellar Weston-Hurst syndrome early treated by craniectomy, steroids and plasma exchange. This is the first case of infratentorial Weston-Hurst syndrome associated with a favorable outcome 1).
1)
Bonduelle T, Stricker J, Minéo JF, Massri A, Guesdon C, Barroso B, Bonnan M.
Weston-Hurst syndrome with acute hemorrhagic cerebellitis. Clin Neurol Neurosurg.
2018 Aug 11;173:118-119. doi: 10.1016/j.clineuro.2018.08.007. [Epub ahead of
print] PubMed PMID: 30121019.