Spinal cord hemangioblastoma epidemiology

Spinal cord hemangioblastomas are the third most common spinal cord tumor, representing 2-6% of all intramedullary tumors.

Haemangioblastomas are mostly sporadic (two thirds) with a peak presentation in the fourth decade. Sporadic haemangioblastomas only rarely occur in children. Males and females are affected equally 4,7.

One third of patients with haemangioblastomas (not just spinal) have von Hippel-Lindau syndrome 6-7 and typically these patients present earlier with multiple tumours.