Orbital schwannoma is a rare type of peripheral nerve sheath tumor (PNST) that varies in clinical presentation. Orbital schwannomas typically involve the head and neck, and rarely occur within the orbit. Other tumor types within this family include neurofibromas and malignant PNSTs, which are more commonly seen in patients with neurofibromatosis (NF). Orbital involvement is seen in 11-28% of patients with NF-1 or a family history of NF, however, the risk of specifically developing orbital schwannoma within those populations is 1.5%