Brain angiolipomas are extremely rare and almost all presented observations describe sellar tumors. On MRI study brain angiolipoma may be mistaken for pituitary neuroendocrine tumor or meningioma but fat saturation sequences and histological examination clear the diagnosis 1) 2) 3) 4).
In those rare cases when angiolipoma is found in cerebral hemispheres, it is important to establish the diagnosis before surgery to plan correct treatment and avoid complications, particularly profound bleeding 5).
Shekhtman et al. presented an untypical case of frontal lobe angiolipoma manifested with seizures and initially described as an arteriovenous malformation.
MRI with a fat-suppression sequence plays a key role in angiolipomas diagnostics. 6).
A patient with Klippel-Feil syndrome and multiple malformations, including tracheoesophageal fistula, bifid thumb and intracranial lipomas/angiolipomas, that have not been previously described in the syndrome, so it is considered an exceptional finding 7).