====== Rippled ventricular wall ====== Severe [[L1 syndrome]]: as in mild L1 syndrome plus anterior [[cerebellar vermis]] hypoplasia, large [[massa intermedia]], enlarged [[quadrigeminal plate]], [[rippled ventricular wall]] following [[ventriculoperitoneal shunt]] placement (pathognomonic for [[X-linked hydrocephalus]]). Profound [[mental retardation]] in virtually all cases