Show pageBacklinksCite current pageExport to PDFBack to top This page is read only. You can view the source, but not change it. Ask your administrator if you think this is wrong. ====== Von Hippel-Lindau disease epidemiology ====== Incidence: 1 in 31,000 to 36,000 live births. ≈ 30% of patients with [[cerebellar hemangioblastoma]] have VHL ((Hottinger AF, Khakoo Y. Neurooncology of familial cancer syndromes. J Child Neurol. 2009; 24:1526–1535)). [[Von Hippel-Lindau disease]] has an incidence of one in 36,000 births. There is over 90% penetrance by the age of 65. Age at diagnosis varies from infancy to age 60–70 years, with average patient age at a clinical diagnosis of 26 years. von_hippel-lindau_disease_epidemiology.txt Last modified: 2024/06/07 02:52by 127.0.0.1